Authors:
Meta Novantisari
and
Damayanti Tinduh
Affiliation:
Universitas Airlangga, Indonesia
Keyword(s):
Spinal cord injury, spinal neurofibromatosis, paraplegia, rehabilitation
Abstract:
Neurofibromatosis is the most commonly inherited disorder affecting the nervous system. This autosomal dominant, neurocutaneous syndrome is associated with multiple tumors of the nervous system, including neurofibromas, schwannomas, meningiomas, and intracranial gliomas. Spinal cord involvement in neurofibromatosis is typically from extramedullary growth of spinal nerve root tumors. A 16-year-old male had weakness in both legs gradually and finally could not move at all. He had sensory deficits as high as dematome T6. He had disturbance of bowel and bladder. He also had severe spasticity. On MRI examination there were multiple intradural extramedular masses at T3 and L5-S1. The patient was operated on for posterior stabilization, laminectomy decompression and Smith Petersen Osteotomy. The patient was diagnosed with T5 paraplegia AIS B ec. Spinal Neurofibromatosis. The rehabilitation program included active breathing exercises, ROM exercises, sensory reeducation, spasticiy inhibition,
CTLSO, and mobilization gradually. The goals for this patient were independent ambulation and improving of sensory deficits and bowel and bladder disturbance. Comprehensive rehabilitation intervention can help patients with spinal cord injury caused by spinal neurofibromatosis to be more functional, and have independent ambulation and ADL
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